Àܵðȸ Çѱ¹±ÙÀ°µð½ºÆ®·ÎÇÇÇùȸ
H > Á¤º¸¸¶´ç > ÀÇ·á¼Ò½Ä
Á¦¸ñ ±ÙÀ°º´ÀÇ 9°¡Áö Á¾·ù ¿ä¾à
ÀÛ¼ºÀÚ °ü¸®ÀÚ µî·ÏÀÏ 2013-05-20
Á¶È¸ 2619
ÆÄÀÏ

±ÙÀ°µð½ºÆ®·ÎÇÇ(Muscular Dystrophies)ÀÇ Á¾·ù

 

±ÙÀ°µð½ºÆ®·ÎÇÇ¿¡´Â µàþ, º¤Ä¿, ¸¶ÀÌ¿ÀÅä´Ð, Áö´ëÇü, ¾È¸é°ß°©Çü°ú ±×¿ÜÀÇ ´Ù¸¥ ¼Ò¼ö ÇüŸ¦ ºñ·ÔÇÑ 12°¡Áö ŸÀÔµéÀÌ ÀÖ´Ù.
±ÙÀ°µð½ºÆ®·ÎÇÇ´Â ¿©·¯ ÇüÅ·Π³ª´©¾îÁö¸ç, ³ªÅ¸³ª´Â Áõ»óÀ̳ª ÁøÇà °úÁ¤Àº °¢±â ´Ù¸£´Ù. ÀÌ Áß¿¡¼­ µà¼¾ÇüÀÌ °¡Àå ½ÉÇÑ ÇüÅÂÀÌ´Ù.

* µà¼¾Çü ±ÙÀ°µð½ºÆ®·ÎÇÇ - Duchenne muscular dystrophy (DMD)
* º¤Ä¿Çü ±ÙÀ°µð½ºÆ®·ÎÇÇ - Becker muscular dystrophy (BMD)
* Áö´ëÇü ±ÙÀ°µð½ºÆ®·ÎÇÇ - Limb girdle dystrophy
* ¾È¸é°ß°©»ó¿ÏÇü ±ÙÀ°µð½ºÆ®·ÎÇÇ - Facioscapulohumeral dystrophy (FSH)
* °ß°©»ó¿ÏÇü ±ÙÀ°µð½ºÆ®·ÎÇÇ - Scapulohumeral muscular dystrophy

* ¼±Ãµ¼º ±ÙÀ°µð½ºÆ®·ÎÇÇ - Congenital muscular dystrophy (CMD)
* ÁßÃ߽Űæ°è ¿¬·ç ¼±Ãµ¼º ±ÙÀ°µð½ºÆ®·ÎÇÇ -Congenital muscular dystrophy with central nervous system involvement (Fukuyama muscular dystrophy)

* Emery-Dreifuss ±ÙÀ°µð½ºÆ®·ÎÇÇ (scapuloperoneal md)
* ´«¿¡ ¹ß»ýµÇ´Â ±ÙÀ°µð½ºÆ®·ÎÇÇ - Ocular muscular dystrophy ´«²¨Ç®ÀÌ ¾Æ·¡·Î ³»·Á¿À°Å³ª ¾È±¸ ¿îµ¿¿¡ °ü°èµÇ´Â ±ÙÀ°¿¡ ¹ß»ýÇÏ´Â [±ÙÀ°µð½ºÆ®·ÎÇÇ]
* ¾È±¸¿Í Àεο¡ ¹ß»ýµÇ´Â ±ÙÀ°µð½ºÆ®·ÎÇÇ - Oculopharyngeal muscular dystrophy
* ´«¿¡ ¹ß»ýµÇ´Â ±ÙÀ°¸¶ºñ ±ÙÀ°µð½ºÆ®·ÎÇÇ Ophthalmoplegic Muscular Dystrophy
* ÆÈ°ú ´Ù¸®¿¡¼­ ³¡ºÎºÐ¸¸ ÈûÀÌ ºüÁö´Â Çü - Distal Muscular Dystrophy

* °­Á÷¼º±ÙÀ°µð½ºÆ®·ÎÇÇ - Myotonic Dystrophy
* ¼±ÃµÀû °­Á÷¼º µð½ºÆ®·ÎÇÇ - Congenital myotonic dystrophy

 

 
´ÙÀ½±Û ¨ç °­Á÷¼º(MYOTONIC)±ÙÀ°µð½ºÆ®·ÎÇÇ 
ÀÌÀü±Û